Encapsulating peritoneal sclerosis: A review of 3 cases.
نویسندگان
چکیده
Mujer con síndrome de Laurence-Moon-Biedl. Inició hemodiálisis (HD) a los 11 años. Recibió su primer trasplante renal al año siguiente, que fracasó por trombosis venosa del injerto. Fue derivada a DP por dificultades de acceso vascular 2 años después. Sufrió varias peritonitis e hiperparatiroidismo grave. Inicialmente, su peritoneo era medio-alto transportador. Tras 12 años en técnica, sufrió nueva peritonitis con infección de túnel y eventración peritoneal por el orificio del catéter. En la radiografías se apreció esclerosis y calcificación del peritoneo, comprimiendo vísceras abdominales. Se trató con antibióticos, retirada del catéter y transferencia a HD. Posteriormente, presentó isquemia aguda en miembro inferior derecho, por obstrucción femoropoplítea. La situación clínica de la paciente desestimó tratamiento quirúrgico y falleció poco después.
منابع مشابه
Successful treatment of encapsulating peritoneal sclerosis with immunosuppressive therapy.
Encapsulating peritoneal sclerosis is a rare, but potentially lethal, complication of peritoneal dialysis. Treatment of patients with encapsulating peritoneal sclerosis is controversial. Conservative treatment carries a poor outcome, and immunosuppressive drugs are now used frequently. Most commonly, these immunosuppressive regimens include steroids with or without azathioprine or cyclosporine....
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BACKGROUND Encapsulating peritoneal sclerosis (EPS) is classically described as progressive sclerosis and cocooning of the entire peritoneum; however, there has been limited number of reported cases of localized fibrosis as a variant form. CASE PRESENTATION We describe two cases of acute bowel obstruction with isolated transition points in the setting of long-term peritoneal dialysis. CONCL...
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OBJECTIVES Encapsulating peritoneal sclerosis is a rare but serious complication in patients undergoing peritoneal dialysis. Its mortality rate is approximately 30%, despite treatment with total parenteral nutrition, surgery, tamoxifen, or immunosuppressants. MATERIALS AND METHODS Of 991 kidney transplants performed at our institution over 9 years, 50 patients were treated for chronic periton...
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Encapsulating peritoneal sclerosis (EPS) is a rare but serious complication of peritoneal dialysis (PD). This review discusses the current understanding of the aetiology and pathogenesis of EPS, highlighting histological features which differentiate it from simple sclerosis of the peritoneal membrane which develops with time on PD. Diagnostic criteria are presented, including the role of imagin...
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INTRODUCTION Encapsulating peritoneal sclerosis is a pathological entity mainly associated with peritoneal dialysis (PD). The clinical syndrome is characterized by various degrees of intestinal obstruction due to thickening, sclerosis and calcification of peritoneum resulting in the encapsulation and cocooning of the bowel. It is a rare but potentially devastating complication associated with a...
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BACKGROUND Studies report variation in the incidence and outcomes of encapsulating peritoneal sclerosis (EPS). This study reports the incidence and outcome of EPS cases in a national cohort of peritoneal dialysis (PD) patients. METHODS The incident cohort of adult patients who started PD between 1 January 2000 and 31 December 2007 in Scotland (n = 1238) was identified from the Scottish Renal ...
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عنوان ژورنال:
- Nefrologia : publicacion oficial de la Sociedad Espanola Nefrologia
دوره 35 6 شماره
صفحات -
تاریخ انتشار 2015